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file:///C:/1076188C/down_medical_files/slide0001.htm Content-Transfer-Encoding: quoted-printable Content-Type: text/html; charset="us-ascii" DOWN SYNDROME: FROM THE DOCTOR’S POINT OF VIEW
DOWN SYNDROME:
FROM= THE DOCTOR’S POINT OF VIEW
Dr. Arun Mukherjee, MD
Director & Founder Trustee
On behalf of TEAM - UDAAN <= /span>
UD= AAN for the Differently Abled
A-59 Kailash Colony, New Delhi 100019
www.udaan.org
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Down Syndrome:
a genetic fait ac= ompli.
So why think of treatment?
Diabetes and Hypertension are also genetic fait accomplii”
Don’t we treat them?
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charset="us-ascii" DOWN SYNDROME: FROM THE DOCTOR’S POINT OF VIEW
3 of 45
Incidence by Age of Pregnancy
1 /= 25
1 /= 20
45 = and older =
1 /= 40
1 /= 30
44<= /b>
1 /= 50
1 /= 35
43<= /b>
1 /= 65
1 /= 45
42<= /b>
1 /= 85
1 /= 60
41<= /b>
1 /= 100
1 /= 75
40<= /b>
1 / 1= 40
1 /= 100
39<= /b>
1 / 1= 75
1 / 1= 20
38<= /b>
1 / 225
1 / 1= 50
37<= /b>
1 / 275
1 / 2= 00
36<= /b>
1 / 350
1 / 250
35
1 / 500
1 / 325
34
1 / 625
1 / 420
33
1 / 750
----=
32<= span style=3D'font-family:Arial;font-size:71%;text-shadow:none;color:black; mso-special-format:lastCR;display:none'>
1 / 900
----=
30 - 31
1 / 1100 =
----=
25 - 29
1 / 1400 =
----=
20 - 24
1 / 1250 =
----=
15 - 19
Fre= quency of Live Births of
Babies with Down Syndrome
to Normal Births
Fre= quency of Fetuses with Down
Syndrome to Normal Fetuses
at 16 weeks of pregnancy
Age (years)
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mJtce+sic+393e2gMaAAxajvTIB8NlzNVjUfkEIHaTzP1BKZq/LCdb1hKH9H70Kcr40eW5XXE43k abRz//Jer8Va0drjv0jR+eiXgIk5Kw9ac06KRu3e/NLHvwuXaCxebQKTabbnvxEdhT0/wgnBJqe7 BCahaR5jDr4MsjDVSfBiCouGA7EiOa9ocIMfsJw6UJUUe3mFhCMDYSwotK/+jZCFI6DgC7lmF/nR kAnN+5QmBrhDOdgwOD0pXhBTcyNgRKIR+DsiEp8SCydADQ9OFCIU32azKkX2gUuk0B4CtfiJHvYG jJ4A2oPIWEaPNBGNJ/EgombIRtstDXVxDEsjnFXHNB4kj3p8UOP4yId/6RCQcRgkIeEAx0PioAAA Ow== ------=_NextPart_01C86F2E.08983270 Content-Location: file:///C:/1076188C/down_medical_files/slide0011.htm Content-Transfer-Encoding: quoted-printable Content-Type: text/html; charset="us-ascii" DOWN SYNDROME: FROM THE DOCTOR’S POINT OF VIEW
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Possibi= lity of Multiple Medical abnormalities
nG= eneticists (for Diagnosis) and Therapists (for training the child to take his place in society) h= ave the prime responsibility for the Child
nThere is a significant role the medical profession, too <= /b>
nThese children are often born with mu= ltiple physical and metabolic birth defects or develop many rare complications in later life. They must be looked out for by a doctor, and preventive or curative methods adopted in time to help maintain the quality = of life of the child and later adult.
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CNS
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3D"Pediatric=
CNS Problems
nSeizures: i= n 5 - 10%
nNeed not be classical generalised fit= s.
nCould be minor ones as seen in CP. &#= 13;
nRegular Therapists to keep watch and = refer at once
nMost preval= ent in infancy
nAgain in th= e 20s and 30s
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Alzhei= mer's disease –
What is it?
n<= b>The human brain has a network of billions of nerve cells and connections known as synapses.
n<= b>They become non-functional as part of aging.
nSimilar to slow moving traffic whe= n lanes on a highway are blocked
n<= b>Starts to manifest after the age of 65 years, but = could also start earlier. <= /i>
nEarly diagnosis important, as all = mental problems must not be put under umbrella of Down Syndrome
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Alzhei= mer’s Disease –
Some Warning Signs
nR= ecent memory loss or misplacing things
nD= ifficulty in performing familiar tasks or disorientation = of time and place <= /div>
nC= hange in mood or behaviour or personality
nP= roblems with language and abstract thinking
nP= oor or decreased judgment and loss of initiative
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Alzhei= mer’s Disease –
Incidence in Down’s
n= General population: approx 6%
n= Adults with Down's syndrome: 25%.
nMany individuals with Down syndrome = have the changes in the brain associated = with Alzheimer's, but do not necessarily = develop the clinical disorder.=
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CVS & Blood
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Cardiovascular Problems
nHeart problems reported in 30 - 60%
nArrhythmia, fainting episodes, palpitations, or = chest pain secondary to heart lesion &= #13;
nMay need surgical corrections, within 1st=  6 six months.
nSome genetic regions like 21q22.1-q22.3  and 21q22.1-q22.2, may play role in pathogenesis of = Down syndrome, particularly, for mental retardation and/or cardiac defects
n= www.emedicine.com/ped/topic615.htm  last accessed = Jan 24, 2008
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Congenital Heart Disease
nCan occur in 40-50%; often seen in hospitalized ca= ses (62%)
nCommon cause of death in first 2 years of life = ;
nTypes:
nEndocardial cushion defect (43%)
nVentricular septal defect (32%)
nSecundum atrial septal defect (10%)
nTetralogy of Fallot (6%)
nIsolated patent ductus arteriosus (4%)
nAbout 30% of patients have several cardiac defects=
nMost common: PDA (16%) & Pulmonic Stenosis (9%)
nAbout 70% of all endocardial cushion defects associated with Down
n= www.emedicine.com/ped/topic615.htm last accessed 24 Jan 2008
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Immune system
nDisturbed immunity
nRecurrent respiratory and systemic infections
n12-fold increased r= isk of infectious diseases, especially pneumonia, because of impaired cellular immunity
n= www.emedicine.com/ped/topic615.htm last accessed 24 Jan 2008
n
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Leukemia - 1
nRelative risk = of acute leukemia in the first 5 years of life is 56 times that of individuals without Down = = syndrome.
nApprox. 1 in 1= 50 patients develops leukemia.
nCAUTION: Neona= tal leukemoid reactions (ie, pseudoleukemia) are common, and distinguishing this from true leukemia frequently poses a diagnostic challenge.
n= www.emedicine.com/ped/topic615.htm last accessed 24 Jan 2008
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Leukaemia - 2
nMost cases: Acute megakaryoblastic leukaemia
n= 1st three years of life
n= Properly managed, good prognosis
n= Another form of leukaemia also seen in new-borns with Down syndrome, that disappears sponta= neously during the first 2 to 3 months of life.
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Other Systems
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Spinal Deformities –
Atlanto-Axial Instability (AAI)
nFound in approximately 14% of Down's
n= Increased mobility at level of 1st & 2nd vertebrae è compression of the spinal cord.
nNeck pain
nLoss of upper body strength
nChanges in bladder and bowel functioning
nChanges in gait and unusual posturing of the head & neck.=
n= Majority of the 14% will be asymptomatic
n= About 10% (=3D 1% of Down's) likely to experience problems, esp. if involved in sporting activities.
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Physical Abnorma= lities - 1
nShort arms and legs
n= More difficult to learn sitting because they cannot lean forward and use their arms to prop them up
n= When falling, they fall further before being able to catch themselves
n= Climbing more difficult due to short legs
n= Usually learn to walk at 24 months rather than at the average 12 months.
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Physical Abnorma= lities - 2
nD= ecreased muscle strength
nChild locking their knee when standin= g.
nI= ncreased flexibility in the joints, esp. hips
nI= nstability makes it harder for child to balance.
nH= ypotonia:  diminishes over time but will per= sist throughout life=
nCompensatory but abnormal postures and stance
nHence need f= or DAILY Expert Occupational Therapy
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Abdominal / Genito-Urinary Disease
nGastro-Intestinal System (12%):
nDuodenal atresia or stenosis, Hirschsprung disease (<1%), TE fistula, Meckel diverticulum, imperforate anus, umbilical hernia, etc.
nCeliac Disease in 5-15%
nCan occur in genetically susceptible individuals, specifically those who h= ave the HLA heterodimers DQ2 (observed in 86-100% of individuals with celiac disease) and DQ8. = ;
nThese are strong linkages with high sensitivity an= d poor specificity.
nGenitourinary tract:
nRenal malformations, hypospadias, micropenis, and cryptorchidism occur.
n= www.emedicine.com/ped/topic615.htm last accessed 24 Jan 2008
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Dental Problems<= /span>
nTeeth usually come through late and in an unusual order. nSome teeth can be missing and those that are present can be small and misshapen.
<= span style=3D'font-style:normal'>nBecause the mouth is small cr= owding can occur.
nProblems with gingivitis and periodontal disease.
<= span style=3D'font-style:normal;text-shadow:none'>nYearly Dental Check-up &am= p; Management
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EYE & ENT Pr= oblems
nE= yes:
nCongenital cataracts à= ; blindness if not treated early. = ;
nBlepharitis, Conjunctivitis
nE= NT:
nObstructed airways leading to snoring, unusual sleeping problems and sinusitis.
nHearing Loss is a significant concern
nF= or some the loss may not occur until their teens leading to misdiagnosed behavioural disturbances= .
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Endocrine Proble= ms
nThyroid problems signific= antly increased, affecting growth and cognitive functioning.
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Management
Conventional Interventions
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Physical therapy=
nT= hese children will walk at 24 months even without = OT/PT
n<= b>Early OT/PT can help avoid abnormal compen= satory = postures / gait / stance <= /span>
nU= ntreated, these can significantly impair adult QOL
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Speech and Langua= ge therapy
nHigh ris= k of developing speech and language problem= s
nHearing defects can be a fac= tor
nCan also arise from poor development of muscles of speech production, large tongue & small oral cavity.
<= /span>
nTherapist should focus on exercising= the muscles of speech production as well as focussing on memory and understanding= .
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Modern High Fund= a
nFor long considered just a genetic disorder, where nothing can be done to improve CNS function.
nIn desperation, some experimental avenues a= re being investigated
nWARNING: EXPERIMENTAL AVENUES
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